Congenital Disorders Hypoplastic Left Heart Syndrome Diagnosis in ICD-10-CM
Instructor
Beth Martilik, MA, RHIA, CDIP, CCSDescription
Congenital Disorder Coding: Hypoplastic Left Heart Syndrome Diagnosis (ICD-10-CM) is an online, self-paced course for inpatient, outpatient, and professional fee coders who assign diagnosis codes for complex congenital heart conditions. This course provides a focused review of hypoplastic left heart syndrome, including its clinical presentation, underlying pathophysiology, and the staged surgical approach used for palliation. Coders will learn how ICD-10-CM classifies HLHS across a patient’s lifetime and how to apply official guidelines for congenital malformations accurately and consistently. Designed to support confident diagnosis coding, the course helps coders strengthen accuracy and documentation alignment when coding HLHS.
Included Lessons:
- What is Hypoplastic Left Heart Syndrome?
- Blood Flow from Heart to Lungs
- Surgical Treatment
- ICD-10-CM Coding
- ICD-10-CM Official Guidelines for Coding and Reporting
CEUs available for the following credentials:
AHIMA
CCA, CCS, CCS-P, RHIT, RHIA, CDIP, CHDA, CHPS
Key Takeaways
- Comprehensive Understanding of HLHS: They will have a thorough understanding of hypoplastic left heart syndrome, including its anatomy, pathophysiology, and clinical presentation.
- Surgical Procedures Knowledge: They will gain insight into the staged reconstructive procedures used in the treatment of HLHS, including the Norwood, Glenn, and Fontan procedures, enabling them to accurately code for these interventions.
- ICD-10-CM Coding Proficiency: Coders will develop proficiency in assigning the appropriate ICD-10-CM codes for hypoplastic left heart syndrome, ensuring accurate documentation and billing in medical records.
- Excludes1 Notes Comprehension: They will understand how to navigate Excludes1 notes and index entries to determine which conditions are included in HLHS and which should be coded separately.
Benefits of Taking this Course
- Improved Skills in Accurately Coding Hypoplastic Left Heart Syndrome Cases
- Professional Skill Development
- Increased Clinical Knowledge
- Career Advancement
- Enhanced Coding Accuracy
FAQs
What will I learn about coding hypoplastic left heart syndrome (HLHS) in ICD-10-CM?
This course explains how hypoplastic left heart syndrome is classified in ICD-10-CM and how to accurately assign diagnosis codes for HLHS across the patient’s lifespan. You’ll learn how HLHS is defined, how it differs from other congenital heart defects, and how to apply Chapter 17 guidelines to ensure correct and consistent diagnosis coding.
How does the course help coders apply sequencing and additional code requirements for HLHS?
The course reviews ICD-10-CM sequencing rules for hypoplastic left heart syndrome and explains when additional codes are needed to capture associated cardiac conditions, complications, or surgical status. You’ll learn how to evaluate provider documentation to determine when HLHS is the primary diagnosis and how to report related conditions accurately.
Will this course improve my ability to identify documentation elements needed for accurate HLHS diagnosis coding?
Yes. The course highlights the key documentation details coders must review, including confirmation of the HLHS diagnosis, associated structural abnormalities, and ongoing clinical status. You’ll learn how to interpret cardiology documentation and recognize when clarification may be needed to support compliant ICD-10-CM coding.
About Our Medical Coding Courses
HIAlearn, powered by Health Information Associates (HIA)—a leader in medical coding and auditing for more than three decades—offers a flexible, online education platform designed for today’s coders. With a growing catalog of AHIMA and AAPC-approved coding courses, HIAlearn supports both beginners and experienced coders looking to build confidence, accuracy, and CEU credits.
Courses are available across various coding types including CPT, E/M, ICD-10-CM, and ICD-10-PCS, and are designed for multiple specialties including inpatient, outpatient, profee, and CDI.
To stay up to date, coders can explore our Coding Updates hub for the latest ICD-10-CM, ICD-10-PCS, CPT, and IPPS changes. HIAlearn also supports organizations with group discounts and scalable team access, promoting accuracy, compliance, and continuous professional development across departments.
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Keep learning with more medical coding courses from HIAlearn.
Congenital Disorders Hypoplastic Left Heart Syndrome Norwood Procedure in ICD‑10‑PCS
Prepares you for procedural coding of the initial surgical stage that follows the HLHS diagnosis in the care pathway.
Congenital Disorders Hypoplastic Left Heart Syndrome Bi‑Directional Glenn Procedure in ICD‑10‑PCS
Enables understanding of the intermediate surgical step—critical for accurate sequencing after the Norwood procedure.
Congenital Disorders Hypoplastic Left Heart Syndrome Fontan Procedure in ICD‑10‑PCS
Completes the staged HLHS treatment series in coding—helpful for grasping the full diagnostic-to-procedure continuum.